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Total Colon Aganglionosis is a topic covered in the Pediatric Surgery NaT.

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Hirschsprung disease (HD) is a common cause of lower intestinal obstruction in the newborn. Patients with HD can be classified based on extent of aganglionosis - classical segment disease refers to those with aganglionosis that does not extend beyond the upper sigmoid colon, long segment disease refers to those with aganglionosis extending to the splenic flexure or transverse colon and total colonic aganglionosis (TCA) refers to those in whom the aganglionosis extends to the entire colon and may also extend up to 30 cm proximally into the distal small bowel [1]. Total intestinal aganglionosis, the rarest form, refers to infants with absence of ganglion cells from the duodenum distally. This topic covers the distinct considerations in the management of TCA.

see also Hirschsprung disease for a complete discussion of the entire spectrum of disease

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Last updated: September 7, 2018


Gosain, Ankush, and Andrew Zigman. "Total Colon Aganglionosis." Pediatric Surgery NaT, American Pediatric Surgical Association, 2018. APSA Webapp, www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829568/all/Total_Colon_Aganglionosis.
Gosain A, Zigman A. Total Colon Aganglionosis. In: Waldhausen J, Powell D, Hirschl R, eds. Pediatric Surgery NaT. American Pediatric Surgical Association; 2018. https://www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829568/all/Total_Colon_Aganglionosis. Accessed July 17, 2019.
Gosain, A., & Zigman, A. (2018). Total Colon Aganglionosis. In Waldhausen, J., Powell, D., & Hirschl, R. (Eds.), Pediatric Surgery NaT. Available from https://www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829568/all/Total_Colon_Aganglionosis
Gosain A, Zigman A. Total Colon Aganglionosis [Internet]. In: Waldhausen J, Powell D, Hirschl R, editors. Pediatric Surgery NaT. American Pediatric Surgical Association; 2018. [cited 2019 July 17]. Available from: https://www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829568/all/Total_Colon_Aganglionosis.
* Article titles in AMA citation format should be in sentence-case
TY - ELEC T1 - Total Colon Aganglionosis ID - 829568 A1 - Gosain,Ankush,MD, PhD AU - Zigman,Andrew,MD, CM ED - Waldhausen,John, ED - Powell,David, ED - Hirschl,Ron, Y1 - 2018/09/07/ BT - Pediatric Surgery NaT UR - https://www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829568/all/Total_Colon_Aganglionosis PB - American Pediatric Surgical Association DB - APSA Webapp DP - Unbound Medicine ER -