Thoracic Dystrophy
To view the entire topic, please log in or purchase a subscription.
APSA Pediatric Surgery Library combines Pediatric Surgery Not a Textbook (NaT) with APSA ExPERT, a powerful platform for earning MOC CME credits -- all powered by Unbound Medicine. Explore these free sample topics:
-- The first section of this topic is shown below --
Introduction
Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 as a case report describing a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency [1]. Other noted associations include limb defects and mild dwarfism. Ultimately, short, wide ribs and abnormal costochondral junctions result in a narrow bell-shaped chest.
-- To view the remaining sections of this topic, please log in or purchase a subscription --
Introduction
Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 as a case report describing a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency [1]. Other noted associations include limb defects and mild dwarfism. Ultimately, short, wide ribs and abnormal costochondral junctions result in a narrow bell-shaped chest.
There's more to see -- the rest of this topic is available only to subscribers.