Thoracic Dystrophy
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Introduction
Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 [1]. The case report was of a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency. Patients also have limb defects and mild dwarfism. The short, wide ribs and abnormal costochondral junctions result in a narrow bell shaped chest.
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Introduction
Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 [1]. The case report was of a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency. Patients also have limb defects and mild dwarfism. The short, wide ribs and abnormal costochondral junctions result in a narrow bell shaped chest.
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