Pediatric Surgery NaT is a comprehensive reference for the general surgical care of children. Contains learning objectives, images, videos, and links to MOC CME and the medical literature. Explore these free sample topics:
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Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 . The case report was of a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency. Patients also have limb defects and mild dwarfism. The short, wide ribs and abnormal costochondral junctions result in a narrow bell shaped chest.