Thoracic Dystrophy is a topic covered in the Pediatric Surgery NaT.

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Introduction

Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 as a case report describing a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency [1]. Other noted associations include limb defects and mild dwarfism. Ultimately, short, wide ribs and abnormal costochondral junctions result in a narrow bell-shaped chest.

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Introduction

Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 as a case report describing a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency [1]. Other noted associations include limb defects and mild dwarfism. Ultimately, short, wide ribs and abnormal costochondral junctions result in a narrow bell-shaped chest.

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Last updated: November 14, 2021