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Thoracic Dystrophy

Mark V Mazziotti, MD, Meghna V Misra, MD, Fizan Abdullah, MD, PhD, David Sigalet, MD, PhD, Jamie C Harris, MD
Thoracic Dystrophy is a topic covered in the Pediatric Surgery NaT.

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Introduction

Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 [1]. The case report was of a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency. Patients also have limb defects and mild dwarfism. The short, wide ribs and abnormal costochondral junctions result in a narrow bell shaped chest.

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Last updated: January 16, 2017

Citation

Mazziotti, Mark V, et al. "Thoracic Dystrophy." Pediatric Surgery NaT, American Pediatric Surgical Association, 2017. APSA Webapp, www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829078/all/Thoracic_Dystrophy.
Mazziotti MV, Misra MV, Abdullah F, Sigalet D, Harris JC. Thoracic Dystrophy. In: Waldhausen J, Powell D, Hirschl R, eds. Pediatric Surgery NaT. American Pediatric Surgical Association; 2017. https://www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829078/all/Thoracic_Dystrophy. Accessed May 22, 2019.
Mazziotti, M. V., Misra, M. V., Abdullah, F., Sigalet, D., & Harris, J. C. (2017). Thoracic Dystrophy. In Waldhausen, J., Powell, D., & Hirschl, R. (Eds.), Pediatric Surgery NaT. Available from https://www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829078/all/Thoracic_Dystrophy
Mazziotti MV, Misra MV, Abdullah F, Sigalet D, Harris JC. Thoracic Dystrophy [Internet]. In: Waldhausen J, Powell D, Hirschl R, editors. Pediatric Surgery NaT. American Pediatric Surgical Association; 2017. [cited 2019 May 22]. Available from: https://www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829078/all/Thoracic_Dystrophy.
* Article titles in AMA citation format should be in sentence-case
TY - ELEC T1 - Thoracic Dystrophy ID - 829078 A1 - Mazziotti,Mark,MD AU - Misra,Meghna,MD AU - Abdullah,Fizan,MD, PhD AU - Sigalet,David,MD, PhD AU - Harris,Jamie,MD ED - Waldhausen,John, ED - Powell,David, ED - Hirschl,Ron, Y1 - 2017/01/16/ BT - Pediatric Surgery NaT UR - https://www.pedsurglibrary.com/apsa/view/Pediatric-Surgery-NaT/829078/all/Thoracic_Dystrophy PB - American Pediatric Surgical Association DB - APSA Webapp DP - Unbound Medicine ER -