Thoracic Dystrophy is a topic covered in the Pediatric Surgery NaT.

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Introduction

Asphyxiating thoracic dystrophy, or Jeune syndrome, was first described in 1954 [1]. The case report was of a newborn with a narrow, rigid chest and multiple cartilage anomalies that led to respiratory insufficiency. Patients also have limb defects and mild dwarfism. The short, wide ribs and abnormal costochondral junctions result in a narrow bell shaped chest.

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Last updated: January 16, 2017

Citation

TY - ELEC T1 - Thoracic Dystrophy ID - 829078 A1 - Mazziotti,Mark,MD AU - Misra,Meghna,MD AU - Abdullah,Fizan,MD, PhD AU - Sigalet,David,MD, PhD AU - Harris,Jamie,MD Y1 - 2017/01/16/ PB - Pediatric Surgery NaT UR - https://www.unboundmedicine.com/medline/view/Pediatric-Surgery-NaT/829078/all/Thoracic_Dystrophy ER -