Lymphatic Malformations
Introduction
Welcome to the APSA Quality and Safety Committee Vascular Anomalies Toolkit. This page is intended to help anyone who is interested in Quality Improvement (QI) of the management of patients with vascular anomalies.
Available toolkit projects are listed below. Many of the approaches described are evidence-based - some are not. These approaches have not been approved by APSA.
Please add a header titled "Development of a Vascular Anomalies Clinic"
The treatment of patients with vascular anomalies can be highly specialized and challenging. As such, the development and maintenance of a multidisciplinary vascular anomalies clinic (VAC) is complex. This section intends to provide guidelines and elements that may be helpful in the development of a program to care for such patients. It is a complilation of the efforts of various institutions and organizations, such as Kaiser Permanente Roseville, Children’s Hospital of Los Angeles, and the VASCERN european collaborative.
Protocol:
Resources:
- Vascular Anomalies Classification
- Program Development
- Treatment Algorithms
- Lymphatic Malformations
- Kaiser Permanente Roseville - IR 3-day Sclerotherapy Protocol (Abdominal Lymphatic Malformation)
- CHLA Abdominal Lymphatic Malformation Treatment Algorithm
- CHLA Cervicofacial Lymphatic Malformation Treatment Algorithm
- European Reference Network VASCERN Lymphatic Malformation - Treatment Overview
- European Reference Network VASCERN Simple/Common Lymphatic Malformation - Diagnosis, Management and Treatment
- European Reference Network VASCERN Diffuse/Extensive Lymphatic Malformation - Management and Treatment
- Hemangiomas
- Venous Malformations
- Vascular Anomalies Standard Labs
- Lymphatic Malformations
- Epic Smartphrases
- Clinic Note Templates
- Sample Template for VAC Intake History (for Medical Assistants)
- Kaiser Permanente Roseville - Vascular Anomalies Clinic, Initial Consultation Note
- Kaiser Permanente Roseville - Birthmark and Vascular Anomaly Clinic Note
- Kaiser Permanente Roseville VAC In-Absentia Note
- Kaiser Permanente Roseville In-Absentia Birthmark and VAC Clinic Note
- Kaiser Permanente Roseville - Consult Note, Assessment and Plan for a Vascular Lesion
- Operative Note Templates
- Orders
- Problem List Information and Entries
- Kaiser Permanente Roseville - Infantile Hemangiomas -Timolol & Propanolol Treatment Recommendations for PCPs
- Kaiser Permanente Roseville - Problem List VAC Recommendations Summary
- Smartphrase used to populate a patient’s problem list, which can then be incorporated to the clinic note’s assessment and plan
- Kaiser Permanente Roseville - Problem List VAC In-Absentia Recommendations Summary
- Kaiser Permanente Roseville Problem List VAC Pre-Clinic Review
- Patient Information
- Clinic Note Templates
Stakeholders: Vascular Anomalies Clinic team members
Challenges and solutions:
- Treatment of patients with vascular anomalies can be highly specialized and challenging. As such, development and maintenance of a multidisciplinary vascular anomalies clinic is complex.
Links to published data (used to develop protocol or demonstrating success of protocol):
Submitted by: Doug Miniati, MD
Additional implementers: Jason Sulkowski, MD
Recent Research
References
References
- Engel ER, Hammill A, Adams D, et al. Response to sirolimus in capillary lymphatic venous malformations and associated syndromes: Impact on symptomatology, quality of life, and radiographic response. Pediatr Blood Cancer. 2023;70(4):e30215. [PMID:36651691]
- Ghaffarpour N, Baselga E, Boon LM, et al. The VASCERN-VASCA working group diagnostic and management pathways for lymphatic malformations. Eur J Med Genet. 2022;65(12):104637. [PMID:36223836]
- Greene AK, Liu AS, Mulliken JB, et al. Vascular anomalies in 5,621 patients: guidelines for referral. J Pediatr Surg. 2011;46(9):1784-9. [PMID:21929990]
- Leboulanger N, Bisdorff A, Boccara O, et al. French national diagnosis and care protocol (PNDS, protocole national de diagnostic et de soins): cystic lymphatic malformations. Orphanet J Rare Dis. 2023;18(1):10. [PMID:36639640]
- Mede A, Chotai PN, Huh WJ, et al. Intra-abdominal Cystic Lymphangiomas: The Vanderbilt Experience. J Surg Res. 2023;285:197-204. [PMID:36696706]
- Mehl SC, Kinley A, Todd HF, et al. Institutional Management of Abdominal Lymphatic Malformations: Evolution of Treatment Over a Decade. J Surg Res. 2022;280:296-303. [PMID:36030605]
- Poget M, Fresa M, El Ezzi O, et al. Lymphatic malformations in children: retrospective review of surgical and interventional management. Pediatr Surg Int. 2022;39(1):36. [PMID:36469112]
- Wiegand S, Wichmann G, Dietz A, et al. Association between malformation type, location and functional deficits in lymphatic malformations of the head and neck in children. Eur Arch Otorhinolaryngol. 2023;280(5):2535-2540. [PMID:36695910]
- Zamora AK, Barry WE, Nowicki D, et al. A multidisciplinary approach to management of abdominal lymphatic malformations. J Pediatr Surg. 2021;56(8):1425-1429. [PMID:33526253]
- Zobel MJ, Nowicki D, Gomez G, et al. Management of cervicofacial lymphatic malformations requires a multidisciplinary approach. J Pediatr Surg. 2021;56(5):1062-1067. [PMID:33982660]
- Cardis MA, DeKlotz CMC. Intralesional Deoxycholic Acid Treatment for Fibrofatty Residua of Involuted Infantile Hemangiomas: A Novel Therapeutic Approach. JAMA Dermatol. 2018;154(6):735-737. [PMID:29801031]
- ISSVA Classification of Vascular Anomalies ©2018 International Society for the Study of Vascular Anomalies Available at "issva.org/classification" Accessed March, 2023.